
[内科] 漏斗胸
Can the congenital rachitis of child, have the funnel chest and many place skeleton maldevelopment treat?
孩子先天佝偻病,有漏斗胸和多处骨骼发育不良能治疗吗?
Objective To summarize the short-term efficacy and experience of the non-endoscopic surgical treatment of funnel chest in three incisions.
目的总结无腔镜下三切口手术治疗漏斗胸的近期疗效及经验。
Objective TO review the surgical experience of sternal turnover with rectus muscle pedicle (STO-RMP) and sternal overlapping suture in the treatment of funnel chest and flat chest.
目的总结漏斗胸及扁平胸施行腹直肌蒂胸骨翻转术(STO - RMP)及胸骨重叠术的治疗经验和体会。
Methods 11 cases of funnel-chest deformity were treated by Sternoturnover with pedicle of abdominal rectus muscle and 9 cases were treated with preservating up and down vessel pedicle.
方法应用带腹直肌蒂胸骨翻转术治疗漏斗胸11例,带上下血管蒂胸骨翻转术治疗漏斗胸9例。
漏斗胸(Funnel Chest)是一种先天性胸壁畸形,医学上称为胸骨凹陷(Pectus Excavatum),主要表现为胸骨及相连的肋软骨向内凹陷,形成类似漏斗状的胸腔结构。该症状多见于儿童及青少年,男性发病率高于女性。
临床表现
患者胸骨下部明显向内凹陷,严重时可压迫心脏和肺部,导致呼吸困难、运动耐力下降或心悸。部分患者伴随脊柱侧弯或肋骨异常生长。
病因与机制
研究认为与遗传因素和结缔组织发育异常相关,如胶原蛋白代谢缺陷导致肋软骨过度生长并牵拉胸骨内陷。部分病例与马凡综合征等遗传性疾病有关。
诊断标准
通过胸部CT扫描测量凹陷深度与胸腔横径比值(Haller指数),若指数大于3.25则定义为中重度漏斗胸,需进一步评估心肺功能。
治疗方法
轻症可通过物理矫正训练改善;中重度患者需手术干预,如Nuss微创手术植入矫形钢板,或传统Ravitch手术切除异常肋软骨。
漏斗胸(Funnel Chest),医学上称为Pectus Excavatum,是一种先天性胸壁畸形,其核心特征和相关信息如下:
通过漏斗胸指数(Funnel-Chest Index, FI) 量化评估,公式为:
$$
FI = frac{凹陷横径 times 凹陷纵径 times 凹陷深度}{胸骨长度 times 胸廓横径 times 胸骨角至椎体距离}
$$
如需进一步了解诊断或手术细节,建议参考胸外科权威资料。
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